ICD-10 diagnosis code

E75 Disorders of sphingolipid metabolism and other lipid storage disorders

E75 is the ICD-10 code for Disorders of sphingolipid metabolism and other lipid storage disorders. It is a three-character category divided into 7 subcodes; use the subcode whenever the record supports that level of detail. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.

Code type: Category (3 characters)
Chapter: IV · E00–E90
Classification: WHO ICD-10, 2019 version

What E75 excludes

Conditions that look similar but belong under another code.

mucolipidosis, types I-III E77.0-E77.1
Refsum disease G60.1

Subcodes of E75

E75 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

E75Rubbningar i sfingolipidomsättningen och andra rubbningar i fettupplagringen

DenmarkICD-10-DK

DE75Forstyrrelse i sfingolipidomsætningen og andre lipidaflejringsforstyrrelser

FinlandICD-10-FI

E75Sfingolipidiaineenvaihdunnan häiriöt ja muut rasva-aineiden kertymätaudit

GermanyICD-10-GM

E75Störungen des Sphingolipidstoffwechsels und sonstige Störungen der Lipidspeicherung

FranceICD-10-FR

E75Anomalies du métabolisme des sphingolipides et autres anomalies du stockage des lipides

NetherlandsICD-10-NL

E75stoornissen van sfingolipidenmetabolisme en overige vetstapelingsstoornissen

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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