ICD-10 diagnosis code

N01 Rapidly progressive nephritic syndrome

This page in Swedish

N01 is the ICD-10 code for Rapidly progressive nephritic syndrome. It is a three-character category. WHO defines its fourth-character subdivisions once for the whole group of categories; the national editions below list them in full. It belongs to the block N00–N08 (Glomerular diseases) in Chapter XIV, Diseases of the genitourinary system.

Code type
Category (3 characters)
Chapter
XIV · N00–N99
Classification
WHO ICD-10, 2019 version

What N01 includes

Conditions and terms that are coded here.

  • rapidly progressive:
    • glomerular disease
    • glomerulonephritis
    • nephritis

What N01 excludes

Conditions that look similar but belong under another code.

  • nephritic syndrome NOS N05.-

N01 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

N01Snabbt progredierande glomerulonefrit

  • N01.0Snabbt progredierande glomerulonefrit - lätt glomerulär abnormitet
  • N01.1Snabbt progredierande glomerulonefrit - fokala och segmentella glomerulära skador
  • N01.2Snabbt progredierande glomerulonefrit - diffus membranös glomerulonefrit
  • N01.3Snabbt progredierande glomerulonefrit - diffus mesangiell proliferativ glomerulonefrit
  • N01.4Snabbt progredierande glomerulonefrit - diffus endokapillär proliferativ glomerulonefrit
  • N01.5Snabbt progredierande glomerulonefrit - diffus mesangiokapillär glomerulonefrit
  • N01.6Snabbt progredierande glomerulonefrit - dense deposit disease
  • N01.7Snabbt progredierande glomerulonefrit - diffus crescentisk glomerulonefrit
  • and 2 more national subcodes
NorwayICD-10-NO

Listed through more specific codes:

  • N01.0Raskt progredierende nefrittisk syndrom med mindre glomerulær abnormitet
  • N01.1Raskt progredierende nefrittisk syndrom med fokal eller segmentell glomulusskade
  • N01.2Raskt progredierende nefrittisk syndrom med diffus membranøs glomerulonefritt
  • N01.3Raskt progredierende nefrittisk syndrom med diffus mesangiell proliferativ glomerulonefritt
  • N01.4Raskt progredierende nefrittisk syndrom med diffus endokapillær proliferativ glomerulonefritt
  • N01.5Raskt progredierende nefrittisk syndrom med diffus mesangiokapillær glomerulonefritt
  • N01.6Raskt progredierende nefrittisk syndrom med «dense deposit disease»
  • N01.7Raskt progredierende nefrittisk syndrom med diffus halvmåne-glomerulonefritt
  • and 2 more national subcodes
DenmarkICD-10-DK

DN01Akut progredierende nyrebetændelse

  • DN010Akut progredierende glomerulonefritis med minimale glomerulære forandringer
  • DN011Akut progredierende glomerulonefritis med fokale eller segmentære glomerulære forandringer
  • DN012Akut progredierende glomerulonefritis med diffus membranøs morfologi
  • DN013Akut progredierende glomerulonefritis med diffus mesangial proliferation
  • DN014Akut progredierende glomerulonefritis med diffus endokapillær proliferation
  • DN015Akut progredierende glomerulonefritis med membranoproliferativ morfologi type 1 og 3 eller UNS
  • DN016Akut progredierende glomerulonefritis med membranoproliferativ morfologi type 2
  • DN017Akut progredierende glomerulonefritis med ekstrakapillær morfologi
  • and 2 more national subcodes
GermanyICD-10-GM

N01Rapid-progressives nephritisches Syndrom

FranceICD-10-FR

N01Syndrome néphritique d'évolution rapide

  • N01.70Syndrome néphritique d’évolution rapide avec glomérulonéphrite diffuse en croissant, avec
  • N01.79Syndromes néphritiques d’évolution rapide avec glomérulonéphrite diffuse en croissant,
NetherlandsICD-10-NL

N01snel progressief nefritisch syndroom

United StatesICD-10-CM

Listed through more specific codes:

  • N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
  • N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
  • N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
  • N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
  • N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
  • N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
  • N01.6Rapidly progressive nephritic syndrome with dense deposit disease
  • N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
  • and 3 more national subcodes

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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