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ICD-10 diagnosis code

E76.2 Other mucopolysaccharidoses

This page in Swedish

E76.2 is the ICD-10 code for Other mucopolysaccharidoses. It is a four-character subcategory of E76 (Disorders of glycosaminoglycan metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.

Code type
Subcategory (4 characters)
Chapter
IV · E00–E90
Classification
WHO ICD-10, 2019 version

What E76.2 includes

Conditions and terms that are coded here.

  • Beta-glucuronidase deficiency
  • Mucopolysaccharidosis, types III, IV, VI, VII
  • Syndrome:
    • Maroteaux-Lamy (mild)(severe)
    • Morquio(-like)(classic)
    • Sanfilippo (type B)(type C)(type D)

E76.2 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

E76.2Andra specificerade mukopolysackaridoser

  • E76.2CMaroteaux-Lamys syndrom (lätt)(svår)
  • E76.2DMorquios syndrom
  • E76.2ESanfilippos syndrom (typ B)(typ C)(typ D)
  • E76.2FSlys syndrom
  • E76.2WAndra specificerade mukopolysackaridoser
NorwayICD-10-NO

E76.2Annen mukopolysakkaridose

DenmarkICD-10-DK

DE762Anden mukopolysakkaridose

  • DE762ABeta-glukuronidasemangel
  • DE762BMukopolysakkaridose type VI
  • DE762CMukopolysakkaridose type IV
  • DE762EMukopolysakkaridose type III
  • DE762GMukopolysakkaridose type VII
  • DE762HMukopolysakkaridose type IX
FinlandICD-10-FI

E76.2Muu mukopolysakkaridoosi

GermanyICD-10-GM

E76.2Sonstige Mukopolysaccharidosen

FranceICD-10-FR

E76.2Autres mucopolysaccharidoses

NetherlandsICD-10-NL

E76.2overige gespecificeerde mucopolysaccharidosen

United StatesICD-10-CM

Listed through more specific codes:

  • E76.22Sanfilippo mucopolysaccharidoses
  • E76.29Other mucopolysaccharidoses

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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