E76.1 is the ICD-10 code for Mucopolysaccharidosis, type II. It is a four-character subcategory of E76 (Disorders of glycosaminoglycan metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.
- Code type
- Subcategory (4 characters)
- Chapter
- IV · E00–E90
- Classification
- WHO ICD-10, 2019 version
What E76.1 includes
Conditions and terms that are coded here.
- Hunter syndrome
E76.1 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
E76.1Mukopolysakkaridose, type II
DE761Mukopolysakkaridose type II
E76.1Mukopolysakkaridoosi, tyyppi II
E76.1Mukopolysaccharidose, Typ II
E76.1Mucopolysaccharidose, type II
E76.1mucopolysaccharidose, type II
E76.1Mucopolysaccharidosis, type II
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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