E71.3 is the ICD-10 code for Disorders of fatty-acid metabolism. It is a four-character subcategory of E71 (Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.
- Code type
- Subcategory (4 characters)
- Chapter
- IV · E00–E90
- Classification
- WHO ICD-10, 2019 version
What E71.3 includes
Conditions and terms that are coded here.
- Adrenoleukodystrophy [Addison-Schilder]
- Muscle carnitine palmityltransferase deficiency
- Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency
What E71.3 excludes
Conditions that look similar but belong under another code.
- Schilder disease G37.0
E71.3 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
E71.3Rubbningar i fettsyraomsättningen
- E71.3AKarnitincykel/transportdefekter
- E71.3BBetaoxidationsrubbningar
- E71.3CAcyl-co-enzym A-dehydrogenas-brist
- E71.3DAdrenoleukodystrofi [Addison-Schilder]
E71.3Forstyrrelse i metabolismen av fettsyre
DE713Forstyrrelse i fedtomsætningen
- DE713AAdrenoleukodystrofi (Addison-Schilder)
- DE713BMuskel-karnitinpalmityltransferasemangel
- DE713CAcyl-CoA dehydrogenasemangel
E71.3Rasvahappoaineenvaihdunnan häiriöt
E71.3Störungen des Fettsäurestoffwechsels
E71.3Anomalie du métabolisme des acides gras
E71.3stoornissen van vetzuurmetabolisme
Listed through more specific codes:
- E71.30Disorder of fatty-acid metabolism, unspecified
- E71.32Disorders of ketone metabolism
- E71.39Other disorders of fatty-acid metabolism
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
Look up another code
Stop looking codes up by hand
Docdemic listens to the consultation, writes the note and suggests the diagnosis and procedure codes that fit it, each one checked against your country’s official code list.
Try Docdemic free