ICD-10 diagnosis code

E71.3 Disorders of fatty-acid metabolism

This page in Swedish

E71.3 is the ICD-10 code for Disorders of fatty-acid metabolism. It is a four-character subcategory of E71 (Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.

Code type
Subcategory (4 characters)
Chapter
IV · E00–E90
Classification
WHO ICD-10, 2019 version

What E71.3 includes

Conditions and terms that are coded here.

  • Adrenoleukodystrophy [Addison-Schilder]
  • Muscle carnitine palmityltransferase deficiency
  • Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency

What E71.3 excludes

Conditions that look similar but belong under another code.

E71.3 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

E71.3Rubbningar i fettsyraomsättningen

  • E71.3AKarnitincykel/transportdefekter
  • E71.3BBetaoxidationsrubbningar
  • E71.3CAcyl-co-enzym A-dehydrogenas-brist
  • E71.3DAdrenoleukodystrofi [Addison-Schilder]
NorwayICD-10-NO

E71.3Forstyrrelse i metabolismen av fettsyre

DenmarkICD-10-DK

DE713Forstyrrelse i fedtomsætningen

  • DE713AAdrenoleukodystrofi (Addison-Schilder)
  • DE713BMuskel-karnitinpalmityltransferasemangel
  • DE713CAcyl-CoA dehydrogenasemangel
FinlandICD-10-FI

E71.3Rasvahappoaineenvaihdunnan häiriöt

GermanyICD-10-GM

E71.3Störungen des Fettsäurestoffwechsels

FranceICD-10-FR

E71.3Anomalie du métabolisme des acides gras

NetherlandsICD-10-NL

E71.3stoornissen van vetzuurmetabolisme

United StatesICD-10-CM

Listed through more specific codes:

  • E71.30Disorder of fatty-acid metabolism, unspecified
  • E71.32Disorders of ketone metabolism
  • E71.39Other disorders of fatty-acid metabolism

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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