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ICD-10 diagnosis code

E71.1 Other disorders of branched-chain amino-acid metabolism

This page in Swedish

E71.1 is the ICD-10 code for Other disorders of branched-chain amino-acid metabolism. It is a four-character subcategory of E71 (Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.

Code type
Subcategory (4 characters)
Chapter
IV · E00–E90
Classification
WHO ICD-10, 2019 version

What E71.1 includes

Conditions and terms that are coded here.

  • Hyperleucine-isoleucinaemia
  • Hypervalinaemia
  • Isovaleric acidaemia
  • Methylmalonic acidaemia
  • Propionic acidaemia

E71.1 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

E71.1Andra rubbningar i omsättningen av grenade aminosyror

  • E71.1AHyperleucin-isoleucinemi
  • E71.1BIsovalerisk acidemi
  • E71.1CMetylmalonisk acidemi
  • E71.1DPropionisk acidemi
NorwayICD-10-NO

E71.1Annen forstyrrelse i metabolismen av grenet aminosyre

DenmarkICD-10-DK

DE711Anden forstyrrelse i omsætningen af forgrenede aminosyrer

  • DE711AHyperleucin-isoleucinæmi
  • DE711BHypervalinæmi
  • DE711CIsovalerinacidæmi
  • DE711DMetylmalonacidæmi
  • DE711EPropionacidæmi
FinlandICD-10-FI

E71.1Muu haaraketjuisten aminohappojen aineenvaihdunnan häiriö

GermanyICD-10-GM

E71.1Sonstige Störungen des Stoffwechsels verzweigter Aminosäuren

FranceICD-10-FR

E71.1Autres anomalies du métabolisme des acides aminés à chaine ramifiée

NetherlandsICD-10-NL

E71.1overige gespecificeerde stofwisselingsstoornissen van aminozuren met

United StatesICD-10-CM

Listed through more specific codes:

  • E71.19Other disorders of branched-chain amino-acid metabolism

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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