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ICD-10 diagnosis code

Q87.1 Congenital malformation syndromes predominantly associated with short stature

This page in Swedish

Q87.1 is the ICD-10 code for Congenital malformation syndromes predominantly associated with short stature. It is a four-character subcategory of Q87 (Other specified congenital malformation syndromes affecting multiple systems), the most specific level in the WHO edition. It belongs to the block Q80–Q89 (Other congenital malformations) in Chapter XVII, Congenital malformations, deformations and chromosomal abnormalities.

Code type
Subcategory (4 characters)
Chapter
XVII · Q00–Q99
Classification
WHO ICD-10, 2019 version

What Q87.1 includes

Conditions and terms that are coded here.

  • Syndrome:
    • Aarskog
    • Cockayne
    • De Lange
    • Dubowitz
    • Noonan
    • Prader-Willi
    • Robinow-Silverman-Smith
    • Russell-Silver
    • Seckel
    • Smith-Lemli-Opitz

What Q87.1 excludes

Conditions that look similar but belong under another code.

  • Ellis-van Creveld syndrome Q77.6

Q87.1 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

SwedenICD-10-SE

Q87.1Medfödda missbildningssyndrom som främst är förenade med kortväxthet

  • Q87.1AAarskogs syndrom
  • Q87.1BCockaynes syndrom
  • Q87.1Cde Langes syndrom
  • Q87.1DDubowitz syndrom
  • Q87.1ENoonans syndrom
  • Q87.1FPrader-Willis syndrom
  • Q87.1GRussell-Silvers syndrom
  • Q87.1JSeckels syndrom
  • and 2 more national subcodes
NorwayICD-10-NO

Q87.1Medfødt misdannelsessyndrom som hovedsaklig fører til kortvoksthet

DenmarkICD-10-DK

DQ871Medfødt misdannelsessyndrom med dværgvækst

  • DQ871ACockaynes syndrom
  • DQ871BCornelia de Langes syndrom
  • DQ871CDubowitz' syndrom
  • DQ871DNoonans syndrom
  • DQ871EPrader-Willis syndrom
  • DQ871FRobinow-Silverman-Smiths syndrom
  • DQ871GRussell-Silvers syndrom
  • DQ871HSeckels syndrom
  • and 2 more national subcodes
FinlandICD-10-FI

Q87.1Etenkin lyhytkasvuisuuteen liittyvät synnynnäiset epämuodostumaoireyhtymät

  • Q87.10Aarskogin oireyhtymä
  • Q87.11Cockaynen oireyhtymä
  • Q87.12Cornelia de Langen oireyhtymä
  • Q87.13Dubowitzin oireyhtymä
  • Q87.14Noonanin oireyhtymä
  • Q87.15Prader-Willin oireyhtymä
  • Q87.16Mulibrey-lyhytkasvuisuus
  • Q87.17Russell-Silverin oireyhtymä
  • and 2 more national subcodes
GermanyICD-10-GM

Q87.1Angeborene Fehlbildungssyndrome, die vorwiegend mit Kleinwuchs einhergehen

FranceICD-10-FR

Q87.1Syndromes congénitaux malformatifs associés principalement à une petite taille

NetherlandsICD-10-NL

Q87.1congenitale gestoorde ontwikkelingssyndromen voornamelijk gepaard

United StatesICD-10-CM

Listed through more specific codes:

  • Q87.11Prader-Willi syndrome
  • Q87.19Other congenital malformation syndromes predominantly associated with short stature

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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