Q43.1 is the ICD-10 code for Hirschsprung disease. It is a four-character subcategory of Q43 (Other congenital malformations of intestine), the most specific level in the WHO edition. It belongs to the block Q38–Q45 (Other congenital malformations of the digestive system) in Chapter XVII, Congenital malformations, deformations and chromosomal abnormalities.
- Code type
- Subcategory (4 characters)
- Chapter
- XVII · Q00–Q99
- Classification
- WHO ICD-10, 2019 version
What Q43.1 includes
Conditions and terms that are coded here.
- Aganglionosis
- Congenital (aganglionic) megacolon
Q43.1 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
- Q43.1AHirchsprungs sjukdom (aganglionos) med kort segment
- Q43.1BHirchsprungs sjukdom (aganglionos) med ultrakort segment
- Q43.1XMegakolon, medfödd, UNS
Q43.1Hirschsprungs sykdom
DQ431Medfødt megacolon
- DQ431AMegasigmoideum congenitum
Q43.1Hirschsprungin tauti
Q43.1Hirschsprung-Krankheit
Q43.1Maladie de Hirschsprung
Q43.1ziekte van Hirschsprung
Q43.1Hirschsprung's disease
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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