F84.2 is the ICD-10 code for Rett syndrome. It is a four-character subcategory of F84 (Pervasive developmental disorders), the most specific level in the WHO edition. It belongs to the block F80–F89 (Disorders of psychological development) in Chapter V, Mental and behavioural disorders.
- Code type
- Subcategory (4 characters)
- Chapter
- V · F00–F99
- Classification
- WHO ICD-10, 2019 version
Definition
A condition, so far found only in girls, in which apparently normal early development is followed by partial or complete loss of speech and of skills in locomotion and use of hands, together with deceleration in head growth, usually with an onset between seven and 24 months of age. Loss of purposive hand movements, hand-wringing stereotypies, and hyperventilation are characteristic. Social and play development are arrested but social interest tends to be maintained. Trunk ataxia and apraxia start to develop by age four years and choreoathetoid movements frequently follow. Severe mental retardation almost invariably results.
F84.2 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
F84.2Retts syndrom
F84.2Retts syndrom
DF842Retts syndrom
F84.2Rettin oireyhtymä
F84.2Rett-Syndrom
F84.2Syndrome de Rett
F84.2syndroom van Rett
F84.2Rett's syndrome
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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