E80.0 is the ICD-10 code for Hereditary erythropoietic porphyria. It is a four-character subcategory of E80 (Disorders of porphyrin and bilirubin metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.
- Code type
- Subcategory (4 characters)
- Chapter
- IV · E00–E90
- Classification
- WHO ICD-10, 2019 version
What E80.0 includes
Conditions and terms that are coded here.
- Congenital erythropoietic porphyria
- Erythropoietic protoporphyria
E80.0 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
E80.0Hereditär erytropoetisk porfyri
- E80.0AErytropoetisk protoporfyri
- E80.0BKongenital erytropoetisk porfyri
- E80.0CErytropoetisk koproporfyri
- E80.0WAnnan och ospecificerad hereditär erytropoetisk porfyri
E80.0Arvelig erytropoetisk porfyri
DE800Familiær erytropoietisk porfyri
E80.0Perinnöllinen erytropoieettinen porfyria
E80.0Hereditäre erythropoetische Porphyrie
E80.0Porphyrie érythropoïétique héréditaire
E80.0hereditaire erytropoëtische-porfyrie
E80.0Hereditary erythropoietic porphyria
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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