ICD-10 diagnosis code

E77.0 Defects in post-translational modification of lysosomal enzymes

This page in Swedish

E77.0 is the ICD-10 code for Defects in post-translational modification of lysosomal enzymes. It is a four-character subcategory of E77 (Disorders of glycoprotein metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.

Code type
Subcategory (4 characters)
Chapter
IV · E00–E90
Classification
WHO ICD-10, 2019 version

What E77.0 includes

Conditions and terms that are coded here.

  • Mucolipidosis II [I-cell disease]
  • Mucolipidosis III [pseudo-Hurler polydystrophy]

E77.0 in national editions

Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.

NorwayICD-10-NO

E77.0Defekt i posttranslasjonell modifikasjon av lysosomalt enzym

DenmarkICD-10-DK

DE770Posttranslational defekt i lysosomale enzymer

  • DE770AMukolipidose II
  • DE770BMukolipidose III
FinlandICD-10-FI

E77.0Lysosomaalisten entsyymien translaationjälkeisen muuntumisen virheet

GermanyICD-10-GM

E77.0Defekte der posttranslationalen Modifikation lysosomaler Enzyme

FranceICD-10-FR

E77.0Défauts de la transformation posttraductionnelle des enzymes lysosomiaux

NetherlandsICD-10-NL

E77.0onvolledige modificatie van lysosomale enzymen na translatie

United StatesICD-10-CM

E77.0Defects in post-translational modification of lysosomal enzymes

Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.

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