E70.0 is the ICD-10 code for Classical phenylketonuria. It is a four-character subcategory of E70 (Disorders of aromatic amino-acid metabolism), the most specific level in the WHO edition. It belongs to the block E70–E90 (Metabolic disorders) in Chapter IV, Endocrine, nutritional and metabolic diseases.
- Code type
- Subcategory (4 characters)
- Chapter
- IV · E00–E90
- Classification
- WHO ICD-10, 2019 version
E70.0 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
- E70.0AHyperfenylalaninemi (fenylalaninhydroxylas-brist), total
- E70.0BHyperfenylalaninemi (fenylalaninhydroxylas-brist), partiell
- E70.0XHyperfenylalaninemi (fenylalaninhydroxylas-brist) UNS
E70.0Klassisk fenylketonuri
DE700Klassisk fenylketonuri
E70.0Klassinen fenylketonuria
E70.0Klassische Phenylketonurie
E70.0Phénylcétonurie classique
E70.0klassieke fenylketonurie
E70.0Classical phenylketonuria
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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