D76.1 is the ICD-10 code for Haemophagocytic lymphohistiocytosis. It is a four-character subcategory of D76 (Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue), the most specific level in the WHO edition. It belongs to the block D70–D77 (Other diseases of blood and blood-forming organs) in Chapter III, Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.
- Code type
- Subcategory (4 characters)
- Chapter
- III · D50–D89
- Classification
- WHO ICD-10, 2019 version
What D76.1 includes
Conditions and terms that are coded here.
- Familial haemophagocytic reticulosis
- Histiocytoses of mononuclear phagocytes
D76.1 in national editions
Countries report with their own edition of ICD-10. Most keep the WHO code and add more specific codes beneath it.
D76.1Hemofagocyttær lymfohistiocytose
DD761Hæmofagocytær lymfhistiocytose
- DD761AFamiliær hæmofagocytær retikulose
- DD761BHæmofagocytær lymfohistiocytose, malignitetsassocieret
- DD761CHæmofagocytær lymfohistiocytose, associeret til reumatologisk sygdom
- DD761DHæmofagocytær lymfohistiocytose, reaktiv hæmofagocytisk syndrom
D76.1Hemofagosyyttinen lymfohistiosytoosi
D76.1Hämophagozytäre Lymphohistiozytose
D76.1Lymphohistiocytose hémophagocytaire
D76.1hemofagocytaire lymfohistiocytose
D76.1Hemophagocytic lymphohistiocytosis
Based on the World Health Organization’s International Statistical Classification of Diseases and Related Health Problems, 10th revision (ICD-10), 2019 version, and the national editions published by each country’s health authority. This page is a reference, not coding advice; follow your national coding rules when you report.
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